L-Carnitine (Standard) is the analytical standard for L-Carnitine, intended for research and analytical applications. L-Carnitine hydrochloride ((R)-Carnitine hydrochloride), a highly polar zwitterion, is an essential cofactor for mitochondrial β-oxidation, transporting long-chain fatty acyl-CoAs into mitochondria for degradation. It is an antioxidant and can ameliorate metabolic imbalances in many inborn errors of metabolism.
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